Indolent Wegener's granulomatosis.
نویسندگان
چکیده
Classical Wegener's granulomatosis is a relentlessly progressive and rapidly fatal disease. A pulmonary 'limited form' is associated with a much better prognosis. We report 3 cases of Wegener's granulomatosis which ran a prolonged indolent course despite major manifestations outside the lower respiratory tract and review the literature on survival.
منابع مشابه
Ocular changes in limited forms of Wegener's granulomatosis.
Eight patients who had limited forms of Wegener's granulomatosis are described, with details of their pathology. Ocular pathological data were available for 2 of them. The condition carries a serious ocular risk; useful vision was lost in 6 out of 16 eyes (37%). An indolent but slowly progressive marginal keratitis and scleritis was a prominent feature in 4 patients and was helpful in suggestin...
متن کاملBasilar artery occlusion in a young patient with Wegener's granulomatosis.
BACKGROUND AND PURPOSE Stroke is an uncommon sequela of Wegener's granulomatosis, resulting primarily from vasculitic infiltration of small to medium-sized vessels. We describe a young patient with Wegener's granulomatosis and basilar artery occlusion. CASE DESCRIPTION A 26-year-old man with histopathologically confirmed Wegener's granulomatosis suffered a brain stem stroke 24 hours after ope...
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36 Hind CR, Winearls CG, Lockwood CM, Rees AJ, Pepys MB. Objective monitoring of activity in Wegener's granulomatosis by protein concentration. Clin Nephrol 1984; 21:341-5. 37 Imbach P. Wegener'sche granulomatose. Ergeb Inn Med Kinderheilkd 1977;39:33-54. 38 Lehmann H, Neidermayer W. Stadienteilung der Wegener'schen granulomatose. Med Welt 1987;38: 466-9. 39 Lehmann H, Keifer B. Clinical manife...
متن کاملThe epidemiology of Wegener's granulomatosis. Estimates of the five-year period prevalence, annual mortality, and geographic disease distribution from population-based data sources.
OBJECTIVE To estimate the prevalence, annual mortality, and geographic distribution of Wegener's granulomatosis. METHODS Analysis of national vital statistics data and hospitalization data from a national survey and from all New York State inpatient facilities. RESULTS Between 1979 and 1988, 1,784 death certificates in the United States listed Wegener's granulomatosis as a cause of death. N...
متن کاملProcalcitonin as an indicator of systemic response to infection in active pulmonary Wegener's granulomacytosis.
Differential diagnosis of infection during active immune disease, such as Wegener's granulomatosis (Wegener's granulomatosis), is a major clinical challenge. Laboratory measures, erythrocyte sedimentation rate or C-reactive protein, can be elevated in infections that supervene, or coinciding with, in active Wegener's granulomatosis, and thus are nonspecific. The aim of the study was to compare ...
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ورودعنوان ژورنال:
- Annals of the rheumatic diseases
دوره 42 4 شماره
صفحات -
تاریخ انتشار 1983